L’hémoglobinurie paroxystique nocturne est une maladie liée à une mutation somatique entraînant l’expansion de clones cellulaires déficients pour des. Site Internet de la filière de santé maladies rares MaRIH, Publications Aplasie médullaire/Hémoglobinurie paroxystique nocturne/Anémie de Fanconi. Many translated example sentences containing “hémoglobinurie paroxystique nocturne” – English-French dictionary and search engine for English translations.

Author: Yogami Kajirg
Country: Austria
Language: English (Spanish)
Genre: Marketing
Published (Last): 20 September 2011
Pages: 232
PDF File Size: 7.20 Mb
ePub File Size: 12.84 Mb
ISBN: 272-9-79732-353-6
Downloads: 85972
Price: Free* [*Free Regsitration Required]
Uploader: Mazugrel

Better results in ? The complement inhibitor eculizumab in paroxysmal nocturnal hemoglobinuria. Peffault de Latour et al.

Outcome of aplastic anaemia in children. Multicenter randomized study comparing cyclosporine-A alone and antithymocyte globulin with prednisone for treatment of severe aplastic anemia. Elevated levels of circulating procoagulant microparticles in patients with paroxysmal nocturnal hemoglobinuria and aplastic anemia. Medicine, Jan; 94 1: Change the order of display of the official languages of Canada English first French first Option to display the non-official languages Spanish or Portuguese Paroxystlque Spanish Portuguese Display definitions, contexts, etc.

A rare disorder characterized by hemolysis and hemoglobinuria, the latter accentuated during sleep. Access to the full text of this article requires a subscription. Marchiafava Micheli syndrome Marchiafava-Micheli’s syndrome.

Med Sci Paris ; 25 12 Long-term marrow culture in patients with aplastic anemia compared with marrow transplant recipients and normal controls. Similar outcome of upfront-unrelated and matched sibling stem cell transplantation in idiopathic paediatric aplastic anaemia.

Top of the page – Article Outline. The disease is diagnosed with haemolytic anemia, marrow failure or episodes of venous thrombosis. The treatment of severe acquired aplastic anemia.


Peffault de Latour aZ. Glossaries and vocabularies Access Translation Bureau glossaries and vocabularies.


Thrombotic events are characterized by paroxysgique of unusual sites hepatic, mesenteric, cerebral, dermal veins. Giammarco S et al. A severe and consistent deficit in marrow and circulating primitive hematopoietic cells long-term culture-initiating cells in acquired aplastic anemia. The owners of this website hereby guarantee to respect the legal confidentiality conditions, applicable in France, and not to disclose this data to third parties. Access to the text HTML. In classic PNH, recent studies have focused on inhibiting the complement cascade with encouraging clinical results using eculizumab, a C5-inhibitor humanized monoclonal antibody.

Unrelated cord blood transplantation in patients with idiopathic refractory severe aplastic anemia: Outcome of patients with acquired aplastic anemia given first line bone marrow transplantation or immunosuppressive treatment in the last decade: Transplant results in adults with Fanconi anaemia.

Multicenter phase 3 study of the complement inhibitor eculizumab for the treatment of patients with paroxysmal nocturnal hemoglobinuria.

L’hémoglobinurie paroxystique nocturne – EM|consulte

Antithymocyte globulin with or without cyclosporin A: Natural history of paroxysmal nocturnal haemoglobinuria using modern diagnostic assays. Sicre de Fontbrune et al. In-vivo dominant immune responses in aplastic anaemia: Language Portal of Canada Access a collection of Canadian resources on all aspects of English and French, including quizzes.

Limited heterogeneity of T cell receptor BV usage in aplastic anemia. Lengline E et al. Personal information regarding our website’s visitors, including their identity, is confidential. Recurrent thrombotic events remains even now associated with bad prognosis, whatever the form of the disease. Cesaro S et al. Treatment of aplastic anemia with antilymphocyte globulin and methylprednisolone with or without cyclosporine.


John Libbey Eurotext – Hématologie – Hémoglobinurie paroxystique nocturne

Nouveau cas clinique “Amylose AL” Testez vos connaissances. Evidence for a metabolic shift of arginine metabolism in sickle cell disease. Thromboses remain a major life threatening complication affecting outcomes in both disease subcategories. Access to the PDF text.

There was a problem providing the content you requested

Benajiba L et al. Access a collection of Canadian resources on all aspects of English and French, including quizzes. Prospective randomized multicenter study comparing cyclosporin alone versus the combination of antithymocyte globulin and cyclosporin for treatment hmkglobinurie patients with nonsevere aplastic anemia: Paroxysmal nocturnal hemoglobinuria PNH is a rare acquired disorder of hematopoietic stem cells.

The hematopoietic defect in aplastic anemia assessed by long-term marrow culture. Gene expression profiling in CD34 cells to identify differences between aplastic anemia patients and healthy volunteers.

Oligoclonal and polyclonal CD4 and CD8 lymphocytes in aplastic anemia and paroxysmal nocturnal hemoglobinuria measured by V beta CDR3 spectratyping and flow cytometry. A collection of writing tools that cover the many facets of Paroxgstique and French grammar, style and usage.

In which subject field? Eculizumab in paroxysmal nocturnal hemoglobinuria. Hematopoietic stem cell transplantation in childhood inherited bone marrow failure syndrome.

Author: admin